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Revista médica de Chile

versão impressa ISSN 0034-9887

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SILVA O, Rafael et al. Pulmonary lymphangioleiomyomatosis: Report of one case. Rev. méd. Chile [online]. 2009, vol.137, n.11, pp.1474-1477. ISSN 0034-9887.  http://dx.doi.org/10.4067/S0034-98872009001100010.

Lymphangioleiomyomatosis (LAM) is a rare interstitial lung disease, of unknown etiology, affecting almost exclusively women. Microscopically LAM consists of a diffuse proliferation of smooth muscle cells. LAM can occur without evidence of other diseases (sporadic LAM) or in conjunction with tuberous sclerosis complex (TSC). It presents with progressive breathlessness or with recurrent pneumothorax or chylothorax. We report a 33 year-old woman with a history of recurrent pneumothorax. Computed tomography (CT) scans showed numerous thin-walled cysts throughout the lungs, a characteristic finding in LAM. A pulmonary biopsy was compatible with the diagnosis and HMB-45 monoclonal antibodies were positive. Treatment with Sirolimus was started).

Palavras-chave : Lymphangioleiomyomatosis; Lung diseases; Pneumothorax.

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