SciELO - Scientific Electronic Library Online

 
vol.34 issue2The Study of Cephalic Index in North Indian PopulationA Comparison of the Relationship between the Golden Ratio and Anatomical Characteristics of the Supraorbital Foramen in Bare Skulls Belonging to the Byzantine Era and Modern Era author indexsubject indexarticles search
Home Pagealphabetic serial listing  

Services on Demand

Journal

Article

Indicators

Related links

  • On index processCited by Google
  • Have no similar articlesSimilars in SciELO
  • On index processSimilars in Google

Share


International Journal of Morphology

On-line version ISSN 0717-9502

Abstract

INZUNZA, Oscar et al. Congenital Absence of The Hepatic Portal Vein Associated to Intestinal Malrotation and Left-Sided Inferior Vena Cava: A Case Report. Int. J. Morphol. [online]. 2016, vol.34, n.2, pp.665-670. ISSN 0717-9502.  http://dx.doi.org/10.4067/S0717-95022016000200039.

Congenital absence of the hepatic portal vein is an extremely rare malformation that was first described by John Abernethy in 1793. Only 101 cases had been described in the literature until 2015 and most affected females. In this anomaly, also known as congenital extrahepatic porto-systemic shunt (CEPS), intestinal venous drainage is derived towards the territory of the systemic veins and could be associated with other birth defects, including heart and biliary tract anomalies, metabolic diseases, mental retardation. We present the case of a 2-year-old boy who died because of multifocal pneumonia and necropsy showed anatomical findings consistent with this malformation as an incidental finding. The portal vein followed an anomalous course and joined the right renal vein, forming the "mesenteric-splenic-renal" venous collector, which then received the right gonadal vein and ended at the confluence of the common iliac veins. In our case this anomaly was associated to intestinal malrotation, aberrant hepatic artery and persistent left inferior vena cava, situation described once in the literature. The finding of these anatomical abnormalities in cadavers has a great teaching value for our undergraduate and graduate students who are learning anatomy and they can also assess the associated clinical.

Keywords : Absence of portal vein; Porto-caval anastomosis; Portal vein development; Intestinal malrotation.

        · abstract in Spanish     · text in Spanish     · Spanish ( pdf )

 

Creative Commons License All the contents of this journal, except where otherwise noted, is licensed under a Creative Commons Attribution License