SciELO - Scientific Electronic Library Online

 
vol.34 número2Estudio de Índice Cefálico en una Población del Norte de IndiaComparación de la Relación entre la Proporción Áurea y las Características Anatómicas del Foramen Supraorbitario en Cráneos de la Época Bizantina y la Edad Moderna índice de autoresíndice de materiabúsqueda de artículos
Home Pagelista alfabética de revistas  

Servicios Personalizados

Revista

Articulo

Indicadores

Links relacionados

  • En proceso de indezaciónCitado por Google
  • No hay articulos similaresSimilares en SciELO
  • En proceso de indezaciónSimilares en Google

Compartir


International Journal of Morphology

versión On-line ISSN 0717-9502

Resumen

INZUNZA, Oscar et al. Congenital Absence of The Hepatic Portal Vein Associated to Intestinal Malrotation and Left-Sided Inferior Vena Cava: A Case Report. Int. J. Morphol. [online]. 2016, vol.34, n.2, pp.665-670. ISSN 0717-9502.  http://dx.doi.org/10.4067/S0717-95022016000200039.

Congenital absence of the hepatic portal vein is an extremely rare malformation that was first described by John Abernethy in 1793. Only 101 cases had been described in the literature until 2015 and most affected females. In this anomaly, also known as congenital extrahepatic porto-systemic shunt (CEPS), intestinal venous drainage is derived towards the territory of the systemic veins and could be associated with other birth defects, including heart and biliary tract anomalies, metabolic diseases, mental retardation. We present the case of a 2-year-old boy who died because of multifocal pneumonia and necropsy showed anatomical findings consistent with this malformation as an incidental finding. The portal vein followed an anomalous course and joined the right renal vein, forming the "mesenteric-splenic-renal" venous collector, which then received the right gonadal vein and ended at the confluence of the common iliac veins. In our case this anomaly was associated to intestinal malrotation, aberrant hepatic artery and persistent left inferior vena cava, situation described once in the literature. The finding of these anatomical abnormalities in cadavers has a great teaching value for our undergraduate and graduate students who are learning anatomy and they can also assess the associated clinical.

Palabras clave : Absence of portal vein; Porto-caval anastomosis; Portal vein development; Intestinal malrotation.

        · resumen en Español     · texto en Español     · Español ( pdf )

 

Creative Commons License Todo el contenido de esta revista, excepto dónde está identificado, está bajo una Licencia Creative Commons